Abstract. ESTOPINAN REBOLLAR, Ramón; ESTOPINAN CANOVAS, Ramón and PILA PELAEZ, Rafael. Enfermedad de Hirschsprung en un adulto. Rev Col. Resumen. LOMBANA, Luis Jorge y DOMINGUEZ, Luis Carlos. Surgery in adult Hirschsprung’s disease. Rev Col Gastroenterol [online]. , vol, n La enfermedad de Hirschsprung es una enfermedad del intestino grueso (colon). Normalmente, las heces fecales son empujadas a través del colon por.

Author: Kajir Doushicage
Country: Czech Republic
Language: English (Spanish)
Genre: Spiritual
Published (Last): 9 January 2006
Pages: 252
PDF File Size: 15.59 Mb
ePub File Size: 7.47 Mb
ISBN: 567-5-14473-969-7
Downloads: 96379
Price: Free* [*Free Regsitration Required]
Uploader: Jusho

Adult Hirschsprung’s disease diagnosed during forensic autopsy. Hirschsprung’s disease; Congenital megacolon; Fecal incontinence. The key finding in barium enema is the existence of a transition zone “funnel” between distal aganglionic bowel normal or narrow and proximal dilated.

Show more Show less. Barium enema showing megarectum. In our case, we are in a situation of irreversible dilatation of entire colon, so we opted for a total colectomy, restoring intestinal transit by ileo-rectal anastomosis.

Enfermedad de Hirschsprung en un adulto

Enfermedad de Hirschsprung del adulto: It is a rare ve that affects 1: IHC x positive for S in the nerve plexuses. The rest of the colon was also dilated.

The scientific works include the areas of Clinical, Endoscopic, Surgical, and Pediatric Gastroenterology, along with related disciplines. Niger J Clin Pract. General laboratory tests were performed complete blood count, blood chemistry, and TSH and the results were within the normal ranges.


Surgery was recommended, but his family did hirscbsprung give their permission.

The patient reported difficulty for expelling gases, although he expelled stools without pathological products. Nowadays its incidence in adult is unknown as this diagnosis is often overlooked in adult population 4. We include a review of existing literature.

Abdomen was very distended and tympanic, with previous laparotomy scar, painful on palpation diffusely. This congenital disease is usually detected in neonatal period. The principal aim of the journal is to publish original work in the broad field of Gastroenterology, as well as to provide information on the specialty and related areas that is up-to-date and relevant. Gordon PH, Nivatvongs S. CD detection of interstitial cells of Cajal: Bowel sounds were minimal.

Adult segmental Hirschsprung disease. Approximately cases have been reported in literature. There was neuronal dysplasia with scarce presence of ganglion cells on both girschsprung of resection. After 24 hours, the patient presented hemodynamic instability, with severe abdominal pain.

It was decided to perform a total colectomy with ileum-rectal anastomosis. A resection of distal rectal mucosa of the aganglionic segment is performed, maintaining muscular wall of this segment.

The authors declare that there is no conflict of interest.

CT scan was performed, showing signs of peritonitis caused by dehiscence of ileum-rectal suture. Agonglinosis is pathgnomonic for HD.

A transition zone was appreciated in distal sigmoid colon. Annals of Diagnostic Pathology ; Treatment is always surgical.

The frequency of HD at young edges is higher on men, but as the edge grows, it occurs more in women. The age of patients ranges from 10 to 73 years old. Clinical case Female patient, 13 years old, coming from Campo Grande – MS, reports that since birth had intestinal constipation, with mean bowel movements at every days with hardened feces, being followed-up by a pediatrician and in treatment for functional constipation.


Vólvulo en adultos

Then, normal colon is lowered through the aganglionic segment, making an anastomosis at level of Morgagni columns. This factor contributed to the delay in her diagnosis, driving the pediatrician out of a HD hypothesis. The rectal biopsy should be made on the back side of rectum, about 6 cm arultos, and it shows absence of ganglion cells, nerve fibers hyperplasia and an increased level of acetylcholinesterase 7.

Introduction Hirschsprung’s disease HD is a malformation of the large intestine characterized by the absence of ganglion cells in submucosal and myenteric plexus, which produces a functional obstruction and dilatation proximal to the affected segment 1. The disease rarely presents as an enfwrmedad intestinal obstruction.